Parameters | Total (n = 60) | With ILD (n = 10) | Without ILD (n = 50) | P-value |
---|---|---|---|---|
Sex ratio, M/F, (n = 60) | 25/35 (41.6/58.4) | 7/3 | 18/32 | 0.046* |
Consanguinity, (n = 55) (%) | 22 (40) | 3 (42.9) | 19 (39.6) | 0.589 |
Family history of PID, (n = 60) (%) | 5 (8.3) | 1 (10) | 4 (8.0) | 0.612 |
Age, y, median (IQR) | 18.5 (11.75-37.0) | 27.0 (10.75–37.5) | 17.0 (12.0–37.0) | 0.576 |
Age at onset (year), median (IQR) | 6.0 (2.75-11.0) | 6.5 (2.37–16.25) | 5.0 (2.5–11.0) | 0.909 |
Age of diagnosis(year),, median (IQR) | 11.0 (4.0–21.0) | 14.0 (4.0–27.0) | 11.0 (4.75–21.75) | 0.843 |
Age of delayed diagnosis(year),, median (IQR) | 3.9 (0.0-8.5) | 3.8 (0.25–9.45) | 4.0 (0.0-9.1) | 0.980 |
Mortality, n (%) | 5 (8.3) | 4 (40%) | 1 (2%) | 0.02* |